Juvenile xanthogranuloma (JXG) is a benign, normolipaemic, self-healing condition and a type of histiocytosis that occurs most frequently in infants and children, although adults may also be affected. This condition usually presents with a
solitary
or
multiple cutaneous lesions and occasionally with extracutaneous lesions, especially the eye, lung, liver, kidney and pericardium. Histologically, JXG represents an accumulation of histiocytes lacking Birbeck granules (non-Langerhans cell), which
can be
differentiated from the Langerhans cells by specific staining techniques. The lesions may be excised for diagnostic, cosmetic or symptomatic reasons. We report a case of juvenile xanthogranuloma that occurred in the nasal cavity and testis for
the
first
time.
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